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首页  >  重组蛋白  >  Human ACAD8 Recombinant Protein
ACAD8 (基因名), Isobutyryl-CoA dehydrogenase, mitochondrial (蛋白名), ACAD8_HUMAN.
产品名称:

Human ACAD8/ Isobutyryl-CoA dehydrogenase, mitochondrial Recombinant Protein
Isobutyryl-CoA脱氢酶、线粒体

货号:

R2437h

商标:
EIAab®
监管等级:
别名:

Activator-recruited cofactor 42 kDa component, Acyl-CoA dehydrogenase family member 8, ARC42, ACAD-8, IBDH, ARC42, IBD

序列号:
Q9UKU7
来源:
E.coli
种属:
Human
标签:
His
纯度:
>90% by SDS-PAGE
浓度:
Reconstitution Dependent
形态:
Liquid
内毒素水平:
Please contact protein@eiaab.com The technician for more information.
应用:
存储缓冲液:
50mM NaH2PO4, 500mM NaCl Buffer with 500mM Imidazole, 10%glycerol(PH8.0)
存储:
Store at -20°C. (Avoid repeated freezing and thawing.)
研究领域:
-
Human ACAD8 Protein
规格 & 价格: cart
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Human ACAD8 Protein
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产品说明书
说明书: 下载说明书
MSDS: MSDS


R&D 技术数据
更多信息,请参阅手册,或联系我们的技术支持: tech@eiaab.com.
基因位点
Cytogenetic band: 11q25 by HGNC 11q25 by Entrez Gene 11q25 by Ensembl
ACAD8 Gene in genomic location: bands according to Ensembl, locations according to GeneLoc (and/or Entrez Gene and/or Ensembl if different)
基因位点
通用注释


亚单元:
Homotetramer, formed by a dimer of dimers (PubMed:11013134, PubMed:14752098). May be part of the large multiprotein complex ARC/DRIP (PubMed:10235267).


功能:
Isobutyryl-CoA dehydrogenase which catalyzes one of the steps of the valine catabolic pathway (PubMed:11013134, PubMed:12359132, PubMed:16857760). To a lesser extent, is also able to catalyze the oxidation of (2S)-2-methylbutanoyl-CoA (PubMed:11013134, PubMed:12359132).


亚细胞位置:
Mitochondrion


该产品尚未在任何出版物中被引用。

[1].
"Identification of isobutyryl-CoA dehydrogenase and its deficiency in humans."

[2].
"Structures of isobutyryl-CoA dehydrogenase and enzyme-product complex: comparison with isovaleryl- and short-chain acyl-CoA dehydrogenases."

[3].
"Isolated 2-methylbutyrylglycinuria caused by short/branched-chain acyl-CoA dehydrogenase deficiency: identification of a new enzyme defect, resolution of its molecular basis, and evidence for distinct acyl-CoA dehydrogenases in isoleucine and valine metabolism."

[4].
"Isolation and characterisation of a cDNA encoding the precursor for a novel member of the acyl-CoA dehydrogenase gene family."

[5].
"Genetic variants in nuclear-encoded mitochondrial genes influence AIDS progression."

[6].
"Association study of cholesterol-related genes in Alzheimer's disease."

[7].
"Variations in IBD (ACAD8) in children with elevated C4-carnitine detected by tandem mass spectrometry newborn screening."

[8].
"Complete sequencing and characterization of 21,243 full-length human cDNAs."

[9].
"The status, quality, and expansion of the NIH full-length cDNA project: the Mammalian Gene Collection (MGC)."

[10].
"Isobutyryl-CoA dehydrogenase deficiency: isobutyrylglycinuria and ACAD8 gene mutations in two infants."
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